US2022363675A1PendingUtilityA1

Novel Ferroportin Inhibitors

71
Assignee: VIFOR INT AGPriority: Oct 23, 2015Filed: Jun 7, 2021Published: Nov 17, 2022
Est. expiryOct 23, 2035(~9.3 yrs left)· nominal 20-yr term from priority
C07D 417/14C07D 495/04C07D 235/14C07D 487/04A61K 31/4184A61P 7/06C07D 401/12Y02A50/30C07D 401/14A61K 31/55A61P 25/00A61K 31/437C07D 471/04A61K 31/4439C07D 413/14A61K 31/4725A61P 3/12A61K 31/506A61K 2300/00A61K 31/497A61P 25/16A61K 31/4709A61K 31/501A61P 7/00C07D 403/14A61K 31/5377A61K 31/4375A61K 31/16A61K 31/427A61K 31/4355A61K 31/4985C07D 413/04A61K 31/4422A61K 31/426A61K 45/06C07D 277/56A61K 31/435C07D 417/12A61K 31/444A61P 25/28A61K 36/9066
71
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Claims

Abstract

The invention relates to novel compounds of the general formula (I),with Het-2 being an optionally substituted bicyclic heteroaryl of the formulapharmaceutical compositions comprising them and the use thereof as medicaments, in particular for the use as ferroportin inhibitors, more particularly for the use in the prophylaxis and/or treatment of diseases caused by a lack of hepcidin or iron metabolism disorders, such as particularly iron overload states such as in particular thalassemia and hemochromatosis.

Claims

exact text as granted — not AI-modified
1 . Compounds according to formula (A-I) 
       
         
           
           
               
               
           
         
         wherein 
         Het-2 is an optionally substituted bicyclic heteroaryl of the formula 
       
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to A 2  and 
         R 4  indicates 1, 2 or 3 optional substituents, which may independently be selected from the group consisting of
 halogen, 
 cyano, 
 optionally substituted alkyl, 
 optionally substituted alkoxy, and 
 a carboxyl group; 
 
         X 1  is C, N, S or O; 
         X 2  is C or N; 
         X 3  is C, N, S or O; and 
         X 4  is C, N, or S 
         with the proviso that 1 to 3 heteroatoms X are present, 
         and wherein X 1 , X 3  and X 4 , when having the meaning of C or N, may carry a further substituent; 
         R 1  is selected from the group consisting of
 hydrogen and 
 optionally substituted alkyl; 
 
         Cycl is selected from the group consisting of
 substituted aryl and 
 substituted or unsubstituted heteroaryl; 
 
         Q is
 hydrogen or 
 C 1 -C 4 -alkyl, which may form a fused 5- or 6-membered ring with Cycl; 
 
         n is 0 or an integer of 1 to 8, preferably n is 0 or 1 to 4, preferably n is 0, 1, 2 or 3; 
         A 1  is
 optionally substituted alkanediyl; 
 
         A 2  is
 optionally substituted alkanediyl or 
 a direct bond; 
 
         R 3  is
 hydrogen, or 
 optionally substituted alkyl; or 
 
         A 1  and R 3  together with the nitrogen atom to which they are bonded form an optionally substituted 4- to 6-membered mono- or bicyclic ring; or 
         R 3  and A 2  together with the nitrogen atom to which they are bonded form an optionally substituted 4- to 7-membered ring; and 
         Y 2  is C or N, wherein
 both Y 2  may be C or 
 one Y 2  may be N and one Y 2  may be C; 
 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         2 . Compounds according to  claim 1 , having the formula (A-II) 
       
         
           
           
               
               
           
         
       
       or pharmaceutically acceptable salts thereof. 
     
     
         3 . Compounds according to  claim 1  or  2 , wherein Cycl is substituted or unsubstituted heteroaryl, or pharmaceutically acceptable salts thereof. 
     
     
         4 . Compounds according to any one of the preceding claims, wherein Cycl is a substituted or unsubstituted heteroaryl, which is selected from a substituted or unsubstituted pyridinyl, forming compounds according to formula (A-IIIa) or (A-IIIb) 
       
         
           
           
               
               
           
         
         wherein 
         R 5  indicates 1 to 4 optional substituents, which may independently be selected from the group consisting of
 halogen, preferably F and Cl, 
 optionally substituted alkyl, preferably methyl, trifluoromethyl, hydroxymethyl, 
 hydroxy, 
 alkoxy, preferably methoxy, 
 an oxo group (═O), forming a substituted pyridinyl-group of the formula 
 
       
       
         
           
           
               
               
           
         
         
           an amino group, such as —NH 2 , mono- or dialkylamino, preferably dialkylamino 
           an aminocarbonyl group, preferably NH 2 —(C═O)—, 
           cyano, and 
           a heterocyclyl group, preferably a morpholinyl-group, 
         
         or pharmaceutically acceptable salts thereof. 
       
     
     
         5 . Compounds according to  claim 4 , having the formula (A-IVa) or (A-IVb) 
       
         
           
           
               
               
           
         
       
       or pharmaceutically acceptable salts thereof. 
     
     
         6 . Compounds according to  claim 4  or  5 , wherein R 5  indicates 1 to 3 substituents, which may independently be selected from the group consisting of
 halogen 
 optionally substituted alkyl, 
 hydroxy, and 
 alkoxy, 
 
       or pharmaceutically acceptable salts thereof. 
     
     
         7 . Compounds according to  claim 6 , wherein R 5  indicates 1 substituent, which is selected from the group consisting of
 halogen   optionally substituted alkyl,   hydroxy, and   alkoxy,   
       or pharmaceutically acceptable salts thereof. 
     
     
         8 . Compounds according to any one of  claims 5  to  7 , having the formula (A-IVc) or (A-IVd) 
       
         
           
           
               
               
           
         
       
       or pharmaceutically acceptable salts thereof. 
     
     
         9 . Compounds according to any one of  claims 5  to  8 , wherein R 5  is selected from the group consisting of
 halogen and 
 optionally substituted alkyl, 
 
       or pharmaceutically acceptable salts thereof. 
     
     
         10 . Compounds according to any one of  claims 5  to  9 , wherein R 5  is selected from a halogen, or pharmaceutically acceptable salts thereof. 
     
     
         11 . Compounds according to  claim 10 , wherein R 5  is selected from Cl and F, preferably R 5  is F, or pharmaceutically acceptable salts thereof. 
     
     
         12 . Compounds according to  claim 1  or  2 , wherein Cycl is an aryl group, which is substituted with 1 to 3 substituents selected from the group consisting of
 hydroxy, 
 halogen, 
 cyano, 
 optionally substituted alkyl, 
 optionally substituted amino, 
 optionally substituted acyl, 
 optionally substituted alkoxy, 
 optionally substituted aryloxy, 
 optionally substituted heterocyclyloxy, 
 optionally substituted aryl, and 
 optionally substituted heterocyclylyl; 
 
       or pharmaceutically acceptable salts thereof. 
     
     
         13 . Compounds according to  claim 12 , wherein Cycl is a substituted phenyl group, forming compounds according to formula (A-Va) or (A-Vb) 
       
         
           
           
               
               
           
         
         wherein R 6  indicates 1, 2 or 3 substitutens which are independently selected from the group consisting of
 hydroxy, 
 halogen, 
 cyano, 
 optionally substituted alkyl, 
 optionally substituted amino, 
 optionally substituted acyl, 
 optionally substituted alkoxy, 
 optionally substituted aryloxy, 
 optionally substituted heterocyclyloxy, 
 optionally substituted aryl, and 
 optionally substituted heterocyclylyl; 
 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         14 . Compounds according to  claim 12  or  13 , wherein R 6  indicates 1 or 2 substituents as defined in  claim 12 ,
 or pharmaceutically acceptable salts thereof. 
 
     
     
         15 . Compounds according to  claim 13  or  14 , wherein R 6  indicates 1 substituent selected from the group as defined in  claim 12 ,
 or pharmaceutically acceptable salts thereof. 
 
     
     
         16 . Compounds according to any one of  claims 13  to  15 , wherein R 6  is selected from the group consisting of
 hydroxy, 
 halogen, preferably F and Cl, 
 cyano, 
 optionally substituted alkyl, 
 optionally substituted amino, such as (—NH 2 ) or mono- or dialkylamino, preferably dimethylamino, 
 optionally substituted alkoxy, preferably methoxy, di-fluoromethoxy and trifluoromethoxy, 
 optionally substituted heterocyclylyl, preferably optionally substituted pyrrolininyl, morpholinyl, and piperazinyl, and 
 an optionally substituted sulfonyl-group, such as preferably heterocyclyl-substituted sulfonyl, preferably of the formula 
 
       
         
           
           
               
               
           
         
       
       or pharmaceutically acceptable salts thereof. 
     
     
         17 . Compounds according to any one of  claims 13  to  16 , wherein R 6  is selected from the group consisting of
 halogen, preferably F, 
 cyano, 
 dimethylamino, 
 methoxy, di-fluoromethoxy and trifluoromethoxy, 
 optionally substituted heterocyclylyl, preferably optionally substituted pyrrolininyl, morpholinyl, and piperazinyl, and 
 an optionally substituted sulfonyl-group, such as preferably heterocyclyl-substituted sulfonyl, preferably of the formula 
 
       
         
           
           
               
               
           
         
       
       or pharmaceutically acceptable salts thereof. 
     
     
         18 . Compounds according to any one of the preceding claims, wherein
 X 1  is N   and wherein one or two further heteroatoms X (X 2 , X 3 , X 4 ) are present, and wherein   X 2  is C or N;   X 3  is C, N, S or 0; and   X 4  is C or N,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         with the proviso that in case of two further heteroatoms both are selected to be N or one is N and one (except X 2 ) is O; 
         and wherein X 3  and X 4 , when having the meaning of C or N, may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         19 . Compounds according to any one of the preceding claims, wherein
 X 1  is N,   X 2  is C and   X 3  is O; and   X 4  is N or C, preferably C,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         and wherein 
         X 4  may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         20 . Compounds according to any one of the preceding claims, wherein
 X 1  is N,   X 2  is C and   X 3  is S; and   X 4  is N or C, preferably C,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         and wherein 
         X 4  may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         21 . Compounds according to any one of the preceding claims, wherein
 X 2  and X 3  are both N,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         and wherein 
         X 1  and X 4  are C; 
         and wherein X 1  and/or X 4  may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         22 . Compounds according to any one of the preceding claims, wherein
 X 1  is C, and   X 2 , X 3  and X 4  are N,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         and wherein 
         X 1  may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         23 . Compounds according to any one of the preceding claims, wherein
 X 1 , X 2  and X 4  are N, and   X 3  is C,   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         and wherein 
         X 3  may carry a further substituent, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         24 . Compounds according to any one of the preceding claims, wherein
 X 1  is O,   X 2  is C,   X 3  is N, and   X 4  is C, and wherein   Y 1  indicates
 hydrogen or 
 an optional subsitutent to X 4 ; 
   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         25 . Compounds according to any one of the preceding claims, wherein
 X 1  is S,   X 2  is C,   X 3  is N, and   X 4  is C, and wherein   Y 1  indicates
 hydrogen or 
 an optional subsitutent to X 4 ; 
   forming a group   
       
         
           
           
               
               
           
         
         wherein * indicates the binding site to the aminocarbonyl-group and ** indicates the binding site to the A 1 -group; 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         26 . Compounds according to any one of the preceding claims, wherein the further substituents of X 1 , X 3  and X 4  are selected from the group consisting of
 halogen, and   optionally substituted alkyl,   
       or pharmaceutically acceptable salts thereof. 
     
     
         27 . Compounds according to  claims 26 , wherein the further substituents of X 1 , X 3  and X 4  are selected from the group consisting of
 Cl, and   linear or branched C 1 -C 3 -alkyl, which may be substituted with 1 to 3 halogens or with a methylene-group; such as preferably a methyl-group, an iso-propyl-group, a CF3-group or a methylene-substituted ethyl-group   
       or pharmaceutically acceptable salts thereof. 
     
     
         28 . Compounds according to any one of the preceding claims, wherein n is 1,
 or pharmaceutically acceptable salts thereof.   
     
     
         29 . Compounds according to any one of the preceding claims, wherein Q is H,
 or pharmaceutically acceptable salts thereof.   
     
     
         30 . Compounds according to any one of the preceding claims, wherein R 1  is H,
 or pharmaceutically acceptable salts thereof.   
     
     
         31 . Compounds according to any one of the preceding claims, wherein Cycl is a group of the formula 
       
         
           
           
               
               
           
         
         wherein * indicates the binding site, 
         or pharmaceutically acceptable salts thereof. 
       
     
     
         32 . Compounds according to any one of the preceding claims, wherein
 A 1  and A 2  are optionally substituted alkanediyl and are the same or different and are independently selected from optionally substituted
 methylene and 
 ethane-1,2-diyl, or wherein 
   A 1  and R 3  together with the nitrogen atom to which they are bonded form an optionally substituted 4-membered aliphatic monocyclic ring;   or pharmaceutically acceptable salts thereof.   
     
     
         33 . Compounds according to any one of the preceding claims, which are selected from 
       
         
           
                 
                 
               
                     
                 
                   Exp. 
                     
                 
                   No. 
                   Structure 
                 
                     
                 
                   1 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   2 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   3 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   4 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   5 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   6 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   7 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   8 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   Exp 
                     
                 
                   No. 
                   Compound 
                 
                     
                 
                   12 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   16 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   19 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   21 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   35 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   36 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   37 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   38 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   39 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   40 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   42 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   43 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   44 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   45 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   46 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   47 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   54 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   55 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   56 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   57 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   58 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   59 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   60 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   61 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   63 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   64 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   65 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   68 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   69 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   70 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   71 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   72 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   74 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   75 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   76 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   77 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   79 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   80 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   81 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   82 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   83 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   84 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   85 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   86 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   87 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   88 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   89 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   90 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   91 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   92 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   93 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   94 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   95 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   96 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   97 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   98 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   99 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   100 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   101 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   102 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   103 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   104 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   105 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   106 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   108 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   109 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   110 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   111 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   112 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   113 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   114 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   115 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   116 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   117 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   118 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   119 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   120 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   121 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   122 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   123 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   124 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   125 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   126 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   127 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   128 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   129 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   131 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   132 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   134 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   135 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   136 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   137 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   138 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   139 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   140 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   141 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   142 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   144 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   145 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   148 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
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                   156 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   157 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
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                   159 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   160 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
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                   162 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   163 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   164 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   165 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
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                   169 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   170 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
                   171 
                   
                     
                       
                       
                           
                           
                       
                     
                   
                 
                     
                 
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       or pharmaceutically acceptable salts thereof. 
     
     
         34 . Compounds according to any one of the preceding claims for the use as a medicament. 
     
     
         35 . Compounds according to any one of the preceding claims for the use as ferroportin inhibitor. 
     
     
         36 . Compounds as defined in any one of the preceding claims for the use in the inhibition of iron transport mediated by ferroportin. 
     
     
         37 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of iron metabolism disorders leading to increased iron levels or increased iron absorption. 
     
     
         38 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of iron overload. 
     
     
         39 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of diseases related to or caused by increased iron levels, increased iron absorption or iron overload. 
     
     
         40 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of diseases associated with ineffective erythropoiesis, such as myelodysplastic syndromes (MDS, myelodysplasia), polycythemia vera and congenital dyserythropoietic anemia. 
     
     
         41 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of diseases caused by reduced levels of hepcidin. 
     
     
         42 . Compounds as defined in any one of the preceding claims for the use in an adjunctive therapy by limiting the amount of iron available to pathogenic microorganisms, such as the bacterium  Vibrio vulnificus,  thereby treating infections caused by said pathogenic microorganisms. 
     
     
         43 . Compounds as defined in any one of the preceding claims for the use according to  claim 39 , wherein the diseases, which are related to or caused by increased iron levels, increases iron absorption or iron overload are selected from thalassemia, hemoglobinopathy, hemoglobin E disease, hemoglobin H disease, haemochromatosis, hemolytic anemia. 
     
     
         44 . Compounds as defined in any one of the preceding claims for the use according to  claim 43 , wherein the thalassemia includes alpha-thalassemia, beta-thalassemia and delta-thalassemia. 
     
     
         45 . Compounds as defined in any one of the preceding claims for the use according to  claim 43 , wherein the hemolytic anemia is sickle cell anemia or congenital dyserythropoietic anemia. 
     
     
         46 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of neurodegenerative diseases such as Alzheimer's disease and Parkinson's disease by limiting the deposition or increase of iron in tissue or cells. 
     
     
         47 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of formation of radicals, reactive oxygen species (ROS) and oxidative stress. 
     
     
         48 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of cardiac, liver and endocrine damage caused by iron overload. 
     
     
         49 . Compounds as defined in any one of the preceding claims for the use in the prophylaxis and/or treatment of inflammation triggered by excess iron. 
     
     
         50 . A medicament containing one or more of the compounds as defined in any one of the preceding claims. 
     
     
         51 . The medicament according to  claim 50  for the use as defined in any one of  claims 35  to  49 . 
     
     
         52 . The medicament according to  claims 50  and  51 , which further contains one or more pharmaceutical carriers and/or auxiliaries and/or solvents. 
     
     
         53 . The medicament according to any one of  claims 50  to  52 , which further contains at least one additional pharmaceutically active compound. 
     
     
         54 . The medicament according to  claim 53 , wherein the at least one additional pharmaceutically active compound is selected from active compounds for the prophylaxis and treatment of iron overload, thalassemia, or haemochromatosis. 
     
     
         55 . The medicament according to  claim 53 , wherein the at least one additional pharmaceutically active compound is selected from active compounds for the prophylaxis and treatment of neurodegenerative diseases, such as Alzheimer's disease or Parkinson's disease, and the associated symptoms. 
     
     
         56 . The medicament according to any one of  claims 50  to  55 , which contains at least one additional pharmaceutically active compound, which is an iron-chelating compound. 
     
     
         57 . The medicament according to any one of  claims 50  to  56 , which is in the form of a formulation for oral or parenteral administration. 
     
     
         58 . Compounds as defined in any one of the preceding claims for the use in a combination therapy, comprising co-administration of the compounds as defined in any of the preceding claims with at least one additional pharmaceutically active compound. 
     
     
         59 . Compounds for the use according to  claim 58 , wherein the co-administration of the combination therapy is carried out in a fixed dose combination therapy by co-administration of the compounds as defined in any of the preceding claims with at least one additional pharmaceutically active compound in a fixed-dose formulation. 
     
     
         60 . Compounds for the use according to  claim 58 , wherein the co-administration of the combination therapy is carried out in a free dose combination therapy by co-administration of the compounds as defined in any of the preceding claims and the at least one additional pharmaceutically active compound in free doses of the respective compounds, either by simultaneous administration of the individual compounds or by sequential use of the individual compounds distributed over a time period. 
     
     
         61 . Compounds for the use according to any one of  claims 58  to  60 , wherein the combination therapy comprises co-administration of the compounds as defined in any of the preceding claims with one or more other pharmaceutically active compounds for reducing iron overload, which are selected from Tmprss6-ASO, iron chelators, curcumin, SSP-004184, Deferitrin, deferasirox, deferoxamine and/or deferiprone. 
     
     
         62 . Compounds for the use according to any one of  claims 58  to  61 , wherein the combination therapy comprises co-administration of the compounds as defined in any of the preceding claims with one or more other pharmaceutically active compounds which are selected from antioxidants, such as n-acetyl cysteine; anti-diabetics, such as GLP-1 receptor agonists; antibiotics, such as vancomycin (Van) or tobramycin; drugs for the treatment of malaria; anticancer agents; antifungal drugs; drugs for the treatment of neurodegenerative diseases such as Alzheimer's disease and Parkinson's disease, comprising dopamine agonists such as Levodopa; anti-viral drugs, such as interferon-α or ribavirin; immunosuppressents, such as cyclosporine A or cyclosporine A derivatives; iron supplements; vitamin supplements; red cell production stimulators; anti-inflammatory biologies; anti-thrombolytics; statins; vasopressors; and inotropic compounds.

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